We use cookies to enhance the usability of our website. If you continue, we'll assume that you are happy to receive all cookies. More information. Don't show this again.
This gene encodes gamma butyrobetaine hydroxylase which catalyzes the formation of L-carnitine from gamma-butyrobetaine, the last step in the L-carnitine biosynthetic pathway. Carnitine is essential for the transport of activated fatty acids across the mitochondrial membrane during mitochondrial beta-oxidation. [provided by RefSeq, Jul 2008]
Enzymes ENZYME proteins Oxidoreductases Predicted intracellular proteins Protein evidence (Ezkurdia et al 2014)
Show all
GO:0005506 [iron ion binding] GO:0005515 [protein binding] GO:0005829 [cytosol] GO:0008270 [zinc ion binding] GO:0008336 [gamma-butyrobetaine dioxygenase activity] GO:0009083 [branched-chain amino acid catabolic process] GO:0016491 [oxidoreductase activity] GO:0016706 [oxidoreductase activity, acting on paired donors, with incorporation or reduction of molecular oxygen, 2-oxoglutarate as one donor, and incorporation of one atom each of oxygen into both donors] GO:0034641 [cellular nitrogen compound metabolic process] GO:0044281 [small molecule metabolic process] GO:0045329 [carnitine biosynthetic process] GO:0055114 [oxidation-reduction process] GO:0070062 [extracellular exosome]
Enzymes ENZYME proteins Oxidoreductases Predicted intracellular proteins Protein evidence (Ezkurdia et al 2014)
Show all
GO:0005506 [iron ion binding] GO:0005515 [protein binding] GO:0005829 [cytosol] GO:0008270 [zinc ion binding] GO:0008336 [gamma-butyrobetaine dioxygenase activity] GO:0009083 [branched-chain amino acid catabolic process] GO:0016491 [oxidoreductase activity] GO:0016706 [oxidoreductase activity, acting on paired donors, with incorporation or reduction of molecular oxygen, 2-oxoglutarate as one donor, and incorporation of one atom each of oxygen into both donors] GO:0034641 [cellular nitrogen compound metabolic process] GO:0044281 [small molecule metabolic process] GO:0045329 [carnitine biosynthetic process] GO:0055114 [oxidation-reduction process] GO:0070062 [extracellular exosome]
Enzymes ENZYME proteins Oxidoreductases Predicted intracellular proteins Protein evidence (Ezkurdia et al 2014)
Show all
GO:0005506 [iron ion binding] GO:0005515 [protein binding] GO:0005829 [cytosol] GO:0008270 [zinc ion binding] GO:0008336 [gamma-butyrobetaine dioxygenase activity] GO:0009083 [branched-chain amino acid catabolic process] GO:0016491 [oxidoreductase activity] GO:0016706 [oxidoreductase activity, acting on paired donors, with incorporation or reduction of molecular oxygen, 2-oxoglutarate as one donor, and incorporation of one atom each of oxygen into both donors] GO:0034641 [cellular nitrogen compound metabolic process] GO:0044281 [small molecule metabolic process] GO:0045329 [carnitine biosynthetic process] GO:0055114 [oxidation-reduction process] GO:0070062 [extracellular exosome]
Enzymes ENZYME proteins Oxidoreductases Predicted intracellular proteins Protein evidence (Kim et al 2014) Protein evidence (Ezkurdia et al 2014)
Show all
GO:0005506 [iron ion binding] GO:0005515 [protein binding] GO:0005739 [mitochondrion] GO:0005829 [cytosol] GO:0008270 [zinc ion binding] GO:0008336 [gamma-butyrobetaine dioxygenase activity] GO:0009083 [branched-chain amino acid catabolic process] GO:0016491 [oxidoreductase activity] GO:0016706 [oxidoreductase activity, acting on paired donors, with incorporation or reduction of molecular oxygen, 2-oxoglutarate as one donor, and incorporation of one atom each of oxygen into both donors] GO:0034641 [cellular nitrogen compound metabolic process] GO:0044281 [small molecule metabolic process] GO:0045329 [carnitine biosynthetic process] GO:0055114 [oxidation-reduction process] GO:0070062 [extracellular exosome]
